Thoracoscopic plication for a huge thoracic meningocele in a patient with Neurofibromatosis
نویسندگان
چکیده
Intrathoracic meningoceles associated with neurofibromatosis type I are rare, and the optimal treatment is still unknown. Herein, we present the case of a 48-year-old Asian female with a huge thoracic meningocele associated with cutaneous neurofibromatosis type I and kyphoscoliosis of the thoracic spine. The large thoracic meningocele was successfully treated through thoracoscopic plication.
منابع مشابه
A Large Intrathoracic Mass in a Patient with Neurofibromatosis-1: a case report
Abstracts: Dural ectasia is circumferential expansion or dilatation of the dural sac, and has been frequently reported in association with type 1 neurofibromatosis (NF1). It should be differentiated from posterior mediastinal tumors such as neurofibroma, neuroblastoma, and ganglioneuroma because NF-1 has a high risk of tumor formation. In the spinal deformities of NF-1 patients, despite the sco...
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